https://www.preprints.org/manuscript/202111.0066
Biallelic pathogenic variants in CLPP, encoding mitochondrial matrix peptidase ClpP cause a rare autosomal recessive condition, Perrault syndrome type 3...
primary accumulationinactivitypeptidaseclppcauses
https://www.ncbi.nlm.nih.gov/Structure/pdb/6WRF
ATP-dependent Clp protease ATP-binding subunit ClpXATP-dependent Clp protease proteolytic subunitGreen fluorescent proteinADENOSINE-5'-DIPHOSPHATEMAGNESIUM...
clpxclppcomplexboundgfp